A 1-year-old boy presents with bilateral (right > left) central corneal opacities with central irido-corneal adhesions on the right and mild microcornea. There appears to be a circular endothelial defect on the back of the corneal scar on the right side. The peripheral corneas are clear. Family and birth history are unremarkable. The child is known to have a heart ventricular septal defect (VSD) awaiting surgery.
Dr. Michelle Lingao, Philippines
Alex V. Levin, MD, MHSc, FRCSC
Chief, Pediatric Ophthalmology and Ocular Genetics
Wills Eye Hospital